Journal of Indian Association of Pediatric Surgeons
Journal of Indian Association of Pediatric Surgeons
                                                   Official journal of the Indian Association of Pediatric Surgeons                           
Year : 2020  |  Volume : 25  |  Issue : 3  |  Page : 178--181

Kaposiform hemangioendothelioma with Kasabach–Merritt phenomenon in a neonate – role of dual therapy: A case report and review of literature


Gaurav Parashar, Gowri Shankar, Ravindra Sahadev, Ramesh Santhanakrishnan 
 Department of Pediatric Surgery, Indira Gandhi Institute of Child Health, South Hospital Complex, Bengaluru, Karnataka, India

Correspondence Address:
Dr. Gowri Shankar
Department of Pediatric Surgery, Indira Gandhi Institute of Child Health, South Hospital Complex, DRC Post, Bengaluru - 560 029, Karnataka
India

Kaposiform hemangioendothelioma (KHE) represents a rare, borderline vascular tumor with locally aggressive behavior. They are often associated with a potentially life-threatening coagulopathy known as Kasabach–Merritt phenomenon (KMP). Due to heterogeneous nature of the vascular lesion and lack of standardized treatment protocols, these patients pose a diagnostic dilemma and therapeutic challenge with morbidity and potential mortality. We report successful management of an infant with KHE and associated KMP. Difficulties encountered in diagnosis, initiation of therapy, and role of dual therapy with vincristine and steroids are discussed.


How to cite this article:
Parashar G, Shankar G, Sahadev R, Santhanakrishnan R. Kaposiform hemangioendothelioma with Kasabach–Merritt phenomenon in a neonate – role of dual therapy: A case report and review of literature.J Indian Assoc Pediatr Surg 2020;25:178-181


How to cite this URL:
Parashar G, Shankar G, Sahadev R, Santhanakrishnan R. Kaposiform hemangioendothelioma with Kasabach–Merritt phenomenon in a neonate – role of dual therapy: A case report and review of literature. J Indian Assoc Pediatr Surg [serial online] 2020 [cited 2021 Jan 18 ];25:178-181
Available from: https://www.jiaps.com/article.asp?issn=0971-9261;year=2020;volume=25;issue=3;spage=178;epage=181;aulast=Parashar;type=0