Journal of Indian Association of Pediatric Surgeons
Journal of Indian Association of Pediatric Surgeons
                                                   Official journal of the Indian Association of Pediatric Surgeons                           
Year : 2018  |  Volume : 23  |  Issue : 4  |  Page : 219--221

Concurrent congenital fibrolipomatous hamartoma and congenital nevus of infancy: A syndromic or chance association


Rajesh Kumar1, Chandni Garg1, Uma Nahar Saikia1, KL N. Rao2 
1 Department of Histopathology, Postgraduate Institute of Medical Education and Research, Chandigarh, India
2 Department of Pediatric Surgery, Postgraduate Institute of Medical Education and Research, Chandigarh, India

Correspondence Address:
Dr. Uma Nahar Saikia
Department of Histopathology, Postgraduate Institute of Medical Education and Research, Chandigarh
India

Congenital nevi and fibrolipomatous hamartoma are benign tumors of childhood, the latter being very uncommon. Fibrous hamartoma of infancy typically occurs in <2 years of life. The concurrence of these two lesions is extremely rare. We report a case of congenital fibrolipomatous hamartoma and congenital nevus of infancy in a 6-month-old male infant. Clinically, a suspicion of benign versus malignant lesion beneath the giant congenital nevus prompted its surgical removal. The histopathology confirmed it to be a compound lesion with benign melanocytic nevi and fascicles of spindle cells with eosinophilic cytoplasm representing hamartoma. Several types of melanocytic combined lesions have been noted with neuroectodermal and mesenchymal components. Sometimes, malignant soft-tissue neoplasm such as liposarcoma, rhabdomyosarcoma, and ganglioneuroblastoma do occur. This case report highlights the role of prompt surgical excision and histopathological examination.


How to cite this article:
Kumar R, Garg C, Saikia UN, N. Rao K L. Concurrent congenital fibrolipomatous hamartoma and congenital nevus of infancy: A syndromic or chance association.J Indian Assoc Pediatr Surg 2018;23:219-221


How to cite this URL:
Kumar R, Garg C, Saikia UN, N. Rao K L. Concurrent congenital fibrolipomatous hamartoma and congenital nevus of infancy: A syndromic or chance association. J Indian Assoc Pediatr Surg [serial online] 2018 [cited 2021 Jan 20 ];23:219-221
Available from: https://www.jiaps.com/article.asp?issn=0971-9261;year=2018;volume=23;issue=4;spage=219;epage=221;aulast=Kumar;type=0