Journal of Indian Association of Pediatric Surgeons
Journal of Indian Association of Pediatric Surgeons
                                                   Official journal of the Indian Association of Pediatric Surgeons                           
Year : 2019  |  Volume : 24  |  Issue : 1  |  Page : 75--77

Two cases of progressive familial intrahepatic cholestasis type 2: Role of surgery with brief review of literature


Hinglaj Saha1, Ghosh Tapanjyoti1, Somak Biswas1, Prafulla Kumar Mishra1, Kalyani Saha Basu1, Uttara Chatterjee2 
1 Department of Paediatric Surgery, Nil Ratan Sircar Medical College and Hospital, Kolkata, West Bengal, India
2 Department of Pathology, IPGMER Medical College and Hospital, Kolkata, West Bengal, India

Correspondence Address:
Dr. Kalyani Saha Basu
B 2/4, Ananda Apartment, 44/1, A J Mistri Lane, Kolkata - 700 027, West Bengal
India

Progressive familial intrahepatic cholestasis (PFIC) is a rare bile acid transporter defect and autosomal recessive disorder with type 2 being the most common type. Partial internal or external biliary diversion delays its progression to end-stage liver disease. Here, we discuss two cases of type 2 PFIC.


How to cite this article:
Saha H, Tapanjyoti G, Biswas S, Mishra PK, Basu KS, Chatterjee U. Two cases of progressive familial intrahepatic cholestasis type 2: Role of surgery with brief review of literature.J Indian Assoc Pediatr Surg 2019;24:75-77


How to cite this URL:
Saha H, Tapanjyoti G, Biswas S, Mishra PK, Basu KS, Chatterjee U. Two cases of progressive familial intrahepatic cholestasis type 2: Role of surgery with brief review of literature. J Indian Assoc Pediatr Surg [serial online] 2019 [cited 2020 Sep 21 ];24:75-77
Available from: http://www.jiaps.com/article.asp?issn=0971-9261;year=2019;volume=24;issue=1;spage=75;epage=77;aulast=Saha;type=0